TY - JOUR AU - Hsu, Chin-Chieh AU - Huang, Tsai-Wang AU - Hsu, Jane-Yi AU - Shin, Nieh AU - Chang, Hung PY - 2013 TI - Malignant peripheral nerve sheath tumor of the chest wall associated with neurofibromatosis: a case report JF - Journal of Thoracic Disease; Vol 5, No 3 (June 26, 2013): Journal of Thoracic Disease Y2 - 2013 KW - N2 - Primary chest wall tumors are relatively rare and represent approximately 5% of all thoracic neoplasms. Malignant peripheral nerve sheath tumor (MPNST) is highly aggressive and occurs in the second or third decade of patients with neurofibromatosis type 1 (NF-1). The estimated incidence of MPNST in patients with NF-1 is 2-5% (general population, 0.001%). This neoplasm usually affects the extremities and rarely the thoracic cavity. We present a case of MPNST of the chest wall in a patient with NF-1 who developed local recurrence 5 months after complete surgical resection and postoperative adjuvant radiotherapy. UR - https://jtd.amegroups.org/article/view/1257